From: Aggressive juvenile fibromatosis of the paranasal sinuses: case report and brief review
Age | Location | Presentation | Pathology | Therapy | Response | Reference |
---|---|---|---|---|---|---|
2 year old male | Right maxillary sinus | Nasal obstruction | Aggressive fibromatosis | Surgical resection | Lost to follow up | [1] |
14 year old female | Right parotid/mandible | Right facial deformity | Aggressive fibromatosis | Surgical resection (positive margins) | No recurrence at < 1 year | [6] |
15 month old male | Nasal cavity/anterior maxilla | Facial deformity | Aggressive fibromatosis | 1. Surgical resection (positive margins) 2. Surgical resection (negative margins) | Recurrence in 1 month, no recurrence | [5] |
2 year old male | Left maxillary sinus | Nasal deformity | Desmoid fibromatosis | Surgical resection (twice), followed by adjuvant tamoxifen | No recurrence at 2 years | [4] |